ARPKD is a rare, monogenic ciliopathy characterized by the formation of bilateral renal cysts and congenital hepatic fibrosis.-The urinary bladder was empty with Foleys catheter in situ, no ascites was seen.last BG: pH: 7.45 PC02: 31.1 HCO3: 22 BE: -11
* Serum Lytes: NA: 133 K: 3.9 Cl: 109
* UA: Leukocytes: 20-23, gravity: 1.015
* BUN: 6 Cr: 0.18
* AST: 96 ALT: 34

- She also had abdominal distention, abdominal U/S was done and showed bilateral medullary nephrocalcinosis and no hepatic hemangiomas.Prenatally, oligohydramnios without any enlargement and/or increased echogenicity of kidneys was observed.