Lakhasly

Left ventricular non-compaction (LVNC) is a rare congenital cardiomyopathy characterized by a "spongy" feature of the myocardium. A thin, com- pacted epicardial layer under an extensive non- compacted endocardial layer can be noticed with the common cardiac image techniques. Prominent trabeculation and deep recesses that communicate with the left ventricular cavity can be visible too. The "spongy" morphologic feature is not charac- teristic only of the left ventricle but can also involve the right ventricle.

Left ventricular non-compaction (LVNC) is a rare congenital cardiomyopathy characterized by a “spongy” feature of the myocardium. A thin, com- pacted epicardial layer under an extensive non- compacted endocardial layer can be noticed with the common cardiac image techniques. Prominent trabeculation and deep recesses that communicate with the left ventricular cavity can be visible too. The “spongy” morphologic feature is not charac- teristic only of the left ventricle but can also involve the right ventricle. This is why talking about “non- compaction cardiomyopathy” seems to be more correct. The non-compaction of the myocardium is a consequence of an abnormal embryonic develop- ment of the ventricular myocardium. During the eighth week of gestation, when the interventricular septum is complete, the increase of ventricular vol- umes is responsible of compression against the tra- beculae of the ventricular walls. This lead to the growth of the compact layer and the organization of some trabeculae in the papillary muscle.
At the same time, intramyocardial vascular- ization develops from the coronary arteries fol- lowing an epicardial to endocardial, base to apex, and septum to side wall direction [1]. For this reason, the non-compaction morphology is more common in the apex, side, and inferior walls of the left ventricle